ORAL AND DENTAL FINDINGS OF A CHILD WITH WEILL-MARCHESANI SYNDROME TYPE II: A CASE REPORT WITH 3-YEAR FOLLOW-UP

نویسندگان

چکیده

Weill-Marchesani syndrome (WMS, OMIM# 227600) is a genetically determined, rare systemic connective tissue disorder. The divided into four types according to mutations in related genes. Given the limited number of individuals with WMS literature, no genotype-phenotype correlations for ADAMTS10, ADAMTS17, FBN1, or LTBP2 have been identified. In accessible none studies were focused on oral and dental anomalies WMS. present case report describes findings 63 months old female patients WMS2.

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ژورنال

عنوان ژورنال: Selcuk dental journal

سال: 2023

ISSN: ['2148-7529']

DOI: https://doi.org/10.15311/selcukdentj.1231513